Abstract: At present, it is not uncommon for patients with biliary dilatation who have failed to undergo multiple operations in clinic. Dong′s classification has a definite guiding significance for choosing appropriate surgical methods. Active hepatectomy with “tailor-made” treatment can cure refractory biliary dilatation involving intrahepatic bile ducts. At present, there are still some controversies about the range of hepatectomy and the management of type D lesions in children. At the same time, we should pay close attention to the long-term complications after dilated bile duct resection.