Abstract: Desmoid tumor of abdominal wall was also known as fibronmatosis of abdominal wall. It is a rare benign fibroblastic tumor, which is characterized by nonenveloped, strong local infiltration, with high recurrence rate after surgery. In December 2011, one patient with huge desmoid tumor of abdominal wall with intestinal tube received surgical resection with singlestage patch repair for the large defect in abdominal wall at the 210th Hospital of PLA, and the result was satisfactory.